Ebstein's anomaly: a rare finding in congenital rubella syndrome.

نویسندگان

  • R Agarwal
  • S S Kothari
چکیده

Ebstein’s anomaly is very rare (0.5 %) cardiac anomaly seen in patient of congenital rubella syndrome. Epidemiology and clinical data are lacking to guide management strategy. Congenital rubella syndrome is manifestation of rubella infection in foetus during period of embryogenesis. A verity of structural heart defect are known to occur with CRS but Ebstein’s anomaly has not been described in association with CRS, but we are reporting case of CRS with EA. The case describe here is 32 year old woman presented with complaint of bilateral pedal oedema was evaluated and diagnosed as having EA. ECG and 2D Echo show right atrial enlargement, septal leaflet detachment and at rialization of right ventricle. Risk of death is increased by having other extra cardiac defects.

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عنوان ژورنال:
  • Indian pediatrics

دوره 38 11  شماره 

صفحات  -

تاریخ انتشار 2001